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Bickerstaff Encephalitis

Names

Description



Patient Groups

Bickerstaff Encephalitis
Bickerstaff's Brainstem Encephalitis

Bickerstaff's brainstem encephalitis (BBE) is an immune disorder of unknown cause. It involves specific anti-bodies that attack parts of the brain. It is characterised by acute, progressive brain dysfunction. Associated with Cerebellar Ataxia. 

Inspire
Encephalitis Society

Bloggers

N/A

Prevalence

The precise incidence and prevalence of BBE is currently unknown. A nationwide survey of patients in Japan with BBE estimated that the annual incidence of BBE affects approximately 100 individuals.
Source: PubMed

Notes:
1. Overlap with other antibody syndromes makes it hard to diagnose and distinguish.
2. Bickerstaff Encephalitis is very rare.

Typical Age of onset

Mostly reported in adults (age range N/A)

Symptoms

  • Double Vision
  • Ataxia (paralysis)
  • Disturbance of consciousness
  • Headache
  • Facial palsy
  • Pupil abnormalities
  • Involuntary eye movements
  • Disturbance of consciousness
  • Overactive reflexes

Source: Mayo Clinic, Healthline

Resources

Link to Clinical Trials
(no active trials at this time)